{"id":4119,"date":"2020-12-29T23:25:39","date_gmt":"2020-12-29T22:25:39","guid":{"rendered":"https:\/\/f101g.org\/bart-loeys-especialista-en-los-sindromes-de-marfan-y-loeys-dietz-galardonado-con-el-premio-nobel-belga-una-primicia-para-las-enfermedades-raras\/"},"modified":"2026-08-11T14:12:24","modified_gmt":"2026-08-11T12:12:24","slug":"bart-loeys-especialista-en-los-sindromes-de-marfan-y-loeys-dietz-galardonado-con-el-premio-nobel-belga-una-primicia-para-las-enfermedades-raras","status":"publish","type":"post","link":"https:\/\/f101g.org\/es\/bart-loeys-especialista-en-los-sindromes-de-marfan-y-loeys-dietz-galardonado-con-el-premio-nobel-belga-una-primicia-para-las-enfermedades-raras\/","title":{"rendered":"Bart Loeys, especialista en los s\u00edndromes de Marfan y Loeys-Dietz, galardonado con el \u00abPremio Nobel belga\u00bb: \u00a1una primicia para las enfermedades raras!"},"content":{"rendered":"<p style=\"text-align: justify;\"><em><strong>El 16 de diciembre de 2020<\/strong>, el profesor Bart Loeys, cardiogen\u00e9tico pedi\u00e1trico de la Universidad de Amberes, especialista de renombre mundial en el s\u00edndrome de Marfan y enfermedades relacionadas (como el s\u00edndrome de Loeys-Dietz), <strong>Copresidente del <a href=\"https:\/\/f101g.org\/es\/la-secuenciacion-genomica-impulsara-la-investigacion-y-contribuira-significativamente-a-la-atencion-a-los-pacientes-por-el-prof-dr-g-g-k-bart-loeys\/\">Comit\u00e9 Cient\u00edfico de la Fundaci\u00f3n 101 Genomas<\/a> y director del <a href=\"https:\/\/f101g.org\/es\/gems-que-es-el-proyecto-gems\/\">proyecto GEMS<\/a><\/strong>, recibi\u00f3 de manos de Su Majestad el Rey el prestigioso premio Francqui 2020<\/em>.<img loading=\"lazy\" decoding=\"async\" class=\"alignright wp-image-1408 size-full\" src=\"https:\/\/f101g.org\/wp-content\/uploads\/2020\/12\/20201216-Bart-recoit-le-prix-Franqui.jpg\" alt=\"\" width=\"768\" height=\"512\"><\/p>\n<p style=\"text-align: justify;\"><strong>Colaur\u00e9at<\/strong>. El profesor Bart Loeys es el ganador, junto con C\u00e9dric Blanpain, de este prestigioso premio, considerado el Nobel belga, que se concede a investigadores destacados en sus campos<a href=\"#_ftn1\" name=\"_ftnref1\">[1<\/a>]. <\/p>\n<p style=\"text-align: justify;\"><strong>Enfermedades raras<\/strong>. Si echa un vistazo a la prestigiosa lista de galardonados, ver\u00e1 que <strong>el profesor Bart Loeys es uno de los pocos, si no el \u00fanico, premiado cuyo trabajo se refiere espec\u00edficamente al campo de las enfermedades raras!&nbsp; <\/strong>  <\/p>\n<p style=\"text-align: justify;\">El profesor Bart Loeys es uno de los principales especialistas mundiales en el s\u00edndrome de Marfan y enfermedades afines, como el s\u00edndrome de Loeys-Dietz, que descubri\u00f3 junto con el profesor Hal Dietz.<\/p>\n<p style=\"text-align: justify;\">Numerosos peri\u00f3dicos han informado de que se le concedi\u00f3 el premio por <em>\u00absu investigaci\u00f3n cl\u00ednica y traslacional que ha llevado a la comprensi\u00f3n, diagn\u00f3stico y tratamiento de enfermedades gen\u00e9ticas humanas que afectan a los vasos sangu\u00edneos&nbsp;<\/em>\u00ab<a href=\"#_ftn2\" name=\"_ftnref2\">[2]<\/a>.<\/p>\n<p style=\"text-align: justify;\">Por lo tanto, este premio le fue concedido por sus investigaciones sobre el s\u00edndrome de Marfan y enfermedades afines (como el s\u00edndrome de Loeys-Dietz), que han contribuido a comprender los mecanismos gen\u00e9ticos que subyacen al da\u00f1o de la aorta. <strong>Mecanismos gen\u00e9ticos que, si se comprenden, podr\u00edan permitir prevenir la rotura a\u00f3rtica, incluso fuera del \u00e1mbito de las enfermedades raras<\/strong><a href=\"#_ftn3\" name=\"_ftnref3\">[3]<\/a>.<\/p>\n<p><strong style=\"text-align: justify;\">Prestigioso palmar\u00e9s<\/strong><span style=\"text-align: justify;\">. El profesor Bart Loeys se une a eminentes galardonados como: Henri Pirenne<\/span><span style=\"text-align: justify;\">Christian de Duve<\/span><span style=\"text-align: justify;\">Ilya Prigogine<\/span><span style=\"text-align: justify;\">Fran\u00e7ois Englert<\/span><span style=\"text-align: justify;\">Mathias Dewatripont<\/span><a style=\"text-align: justify;\" href=\"#_ftn6\" name=\"_ftnref6\"><\/a><span style=\"text-align: justify;\">Philippe Van Parijs<\/span><span style=\"text-align: justify;\">Olivier De Schutter<\/span><a style=\"text-align: justify;\" href=\"#_ftn4\" name=\"_ftnref4\">[4]<\/a><span style=\"text-align: justify;\"> y la prestigiosa lista contin\u00faa<\/span><a style=\"text-align: justify;\" href=\"#_ftn5\" name=\"_ftnref5\">[5<\/a><a style=\"text-align: justify;\" href=\"#_ftn5\" name=\"_ftnref5\">]<\/a><span style=\"text-align: justify;\">&#8230;<\/span><\/p>\n<p style=\"text-align: justify;\"><strong>La petici\u00f3n del Rey<\/strong>. La ceremonia de entrega de premios tuvo lugar en el Palacio de las Academias en un c\u00edrculo muy reducido y siguiendo un protocolo muy estricto debido al COVID19. Durante la ceremonia, los profesores Bart Loeys y C\u00e9dric Blanpain tuvieron la oportunidad de explicar sus respectivas investigaciones a Su Majestad el Rey. El Rey les pregunt\u00f3 entonces si para ellos era imaginable trabajar juntos en un proyecto com\u00fan. El profesor Bart Loeys propuso al profesor C\u00e9dric Blanpain poner su experiencia en c\u00e9lulas madre al servicio del <strong><a href=\"https:\/\/f101g.org\/es\/gems-que-es-el-proyecto-gems\/\">proyecto GEMS<\/a><\/strong>. Esto brind\u00f3 la oportunidad al profesor Bart Loeys de explicar el proyecto GEMS al Rey y al profesor Blanpain. \u00bfContinuar\u00e1?      <\/p>\n<p style=\"text-align: justify;\"><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-1425\" src=\"https:\/\/f101g.org\/wp-content\/uploads\/2020\/12\/12214_253_Dann_Mid-768x512-1-1.jpg\" alt=\"\" width=\"768\" height=\"512\"><\/p>\n<p style=\"text-align: justify;\"><strong>\u00a1Bravo!<\/strong> Por ahora, felicitemos de nuevo al profesor Bart Loeys. Alegr\u00e9monos de la atenci\u00f3n que este prestigioso premio podr\u00e1 atraer sobre la investigaci\u00f3n relativa al s\u00edndrome de Marfan y a las enfermedades relacionadas. Con la esperanza, por \u00faltimo, de que este premio termine de convencer al mayor n\u00famero posible de apoyar financieramente la implicaci\u00f3n del profesor Bart Loeys en <strong><a href=\"https:\/\/f101g.org\/es\/gems-que-es-el-proyecto-gems\/\">el proyecto GEMS llevado por la Fundaci\u00f3n 101 Genomas<\/a><\/strong>.  <\/p>\n<p style=\"text-align: justify;\">\u00a1Enhorabuena Bart y gracias por tu extraordinario trabajo, que da esperanzas a las familias de Marfan y afines&nbsp;!<\/p>\n<p style=\"text-align: right;\"><strong>Ludivine &#038; Romain<\/strong><\/p>\n<p><img loading=\"lazy\" decoding=\"async\" class=\"aligncenter size-full wp-image-1415\" src=\"https:\/\/f101g.org\/wp-content\/uploads\/2019\/10\/CD_2019_10_05_14_33_16.jpg\" alt=\"\" width=\"1200\" height=\"1200\"><\/p>\n<p style=\"text-align: justify;\"><a href=\"#_ftnref1\" name=\"_ftn1\">[1]<\/a> &nbsp;&nbsp;&nbsp;&nbsp;&nbsp; <a href=\"https:\/\/www.vrt.be\/vrtnws\/nl\/2020\/12\/16\/koning-filip-heeft-de-francqui-prijs-uitgereikt\/\" target=\"_blank\" rel=\"noopener noreferrer\">https:\/\/www.vrt.be\/vrtnws\/nl\/2020\/12\/16\/koning-filip-heeft-de-francqui-prijs-uitgereikt\/<\/a><\/p>\n<p style=\"text-align: justify;\"><a href=\"#_ftnref2\" name=\"_ftn2\">[2]<\/a>&nbsp; &nbsp; &nbsp; &nbsp;<a href=\"https:\/\/fondation-francqui.prezly.com\/cedric-blanpain-et-bart-loeys-laureats-2020-des-deux-prix-francqui-collen-en-recherche-fondamentale-et-clinique\" target=\"_blank\" rel=\"noopener noreferrer\">https:\/\/fondation-francqui.prezly.com\/cedric-blanpain-et-bart-loeys-laureats-2020-des-deux-prix-francqui-collen-en-recherche-fondamentale-et-clinique<\/a><\/p>\n<p style=\"text-align: justify;\"><a href=\"#_ftnref3\" name=\"_ftn3\">[3]<\/a>&nbsp; &nbsp; &nbsp; &nbsp; Lea atentamente el informe del jurado:&nbsp;<a href=\"http:\/\/www.francquifoundation.be\/new-page\/prix-francqui\/laureats\/2020-rapport-jury-bart-loeys\/\" target=\"_blank\" rel=\"noopener noreferrer\">http:\/\/www.francquifoundation.be\/new-page\/prix-francqui\/laureats\/2020-rapport-jury-bart-loeys\/<\/a><\/p>\n<p style=\"text-align: justify;\"><a href=\"#_ftnref4\" name=\"_ftn4\">[4]<\/a>       Henri Pirenne (Ciencias Humanas \u2013 Filosof\u00eda y Letras), Christian de Duve (Ciencias Biol\u00f3gicas y M\u00e9dicas \u2013 Qu\u00edmica fisiol\u00f3gica \u2013 Bioqu\u00edmica \u2013 Premio Nobel de Medicina en 1974), Ilya Prigogine (Ciencias Exactas \u2013 Qu\u00edmica y f\u00edsica molecular \u2013 Premio Nobel de Qu\u00edmica en 1977), Fran\u00e7ois Englert (Ciencias Exactas \u2013 F\u00edsica te\u00f3rica \u2013 Premio Nobel de F\u00edsica en 2013), Mathias Dewatripont (Ciencias Humanas \u2013 Ciencias Econ\u00f3micas), Philippe Van Parijs (Ciencias Humanas \u2013 Filosof\u00eda de la Justicia Social), Olivier De Schutter (Ciencias Humanas \u2013 Teor\u00eda de la gobernanza \u2013 Derecho internacional y europeo de los derechos humanos, Derecho de la Uni\u00f3n Europea)<\/p>\n<p style=\"text-align: justify;\"><a href=\"#_ftnref5\" name=\"_ftn5\">[5]<\/a>&nbsp; &nbsp; &nbsp; &nbsp;<a href=\"https:\/\/www.francquifoundation.be\/new-page\/prix-francqui\/laureats\/\" target=\"_blank\" rel=\"noopener noreferrer\">https:\/\/www.francquifoundation.be\/new-page\/prix-francqui\/laureats\/<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>El 16 de diciembre de 2020, el profesor Bart Loeys, cardiogen\u00e9tico pedi\u00e1trico de la Universidad de Amberes, especialista de renombre &hellip;<\/p>\n","protected":false},"author":3,"featured_media":3223,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_jetpack_newsletter_access":"","_jetpack_dont_email_post_to_subs":false,"_jetpack_newsletter_tier_id":0,"_jetpack_memberships_contains_paywalled_content":false,"_jetpack_feature_clip_id":0,"_jetpack_memberships_contains_paid_content":false,"footnotes":"","jetpack_publicize_message":"","jetpack_publicize_feature_enabled":true,"jetpack_social_post_already_shared":false,"jetpack_social_options":{"image_generator_settings":{"template":"highway","default_image_id":0,"font":"","enabled":false},"version":2},"jetpack_post_was_ever_published":false},"categories":[68],"tags":[],"class_list":["post-4119","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-gems-es"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.2 - 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